Uemura, Yuta Tokushima University Tokushima University Educator and Researcher Directory
Kakuta, Nami Tokushima University Tokushima University Educator and Researcher Directory KAKEN Search Researchers
Tanaka, Katsuya Tokushima University Tokushima University Educator and Researcher Directory KAKEN Search Researchers
Methylmalonyl coenzyme A mutase
Background: Methylmalonic acidemia (MMA) is a metabolic disorder of organic acids and is characterized by the accumulation of methylmalonic acids.
Case presentation: The patient was a 19-year-old female diagnosed with severe MMA at 3 days of age, who was scheduled for renal replacement therapy. Preoperatively, there was no evidence of metabolic acidosis or electrolyte abnormalities. Glucose was administered preoperatively following a 6-h fast. Anesthesia was administered using thiamylal, remifentanil, rocuronium, and sevoflurane. After tracheal intubation, the patient underwent an ultrasoundguided bilateral rectus sheath block with ropivacaine. A drop in blood sugar level was treated with 5% glucose. Extubation was performed after intravenous administration of sugammadex.
Conclusions: We report the anesthetic management of a patient with MMA using a combination of general anesthesia and rectus sheath block.
JA Clinical Reports
Japanese Society of Anesthesiologists|Springer Nature
© The Author(s). 2018 Open Access This article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made.
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