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ID 114561
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Keywords
Methylmalonic acidemia
Methylmalonyl coenzyme A mutase
Metabolic acidosis
Content Type
Journal Article
Description
Background: Methylmalonic acidemia (MMA) is a metabolic disorder of organic acids and is characterized by the accumulation of methylmalonic acids.
Case presentation: The patient was a 19-year-old female diagnosed with severe MMA at 3 days of age, who was scheduled for renal replacement therapy. Preoperatively, there was no evidence of metabolic acidosis or electrolyte abnormalities. Glucose was administered preoperatively following a 6-h fast. Anesthesia was administered using thiamylal, remifentanil, rocuronium, and sevoflurane. After tracheal intubation, the patient underwent an ultrasoundguided bilateral rectus sheath block with ropivacaine. A drop in blood sugar level was treated with 5% glucose. Extubation was performed after intravenous administration of sugammadex.
Conclusions: We report the anesthetic management of a patient with MMA using a combination of general anesthesia and rectus sheath block.
Journal Title
JA Clinical Reports
ISSN
23639024
Publisher
Japanese Society of Anesthesiologists|Springer Nature
Volume
4
Start Page
71
Published Date
2018-10-01
Rights
© The Author(s). 2018 Open Access This article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made.
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language
eng
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departments
University Hospital
Medical Sciences