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ID 114388
Author
Takahashi, Mikiko Nippon Medical School
Fukuda, Yuh Nippon Medical School|Itabashi Chuo Medical Center
Morizumi, Shun Tokushima University
Content Type
Journal Article
Description
The patient was a 68-year-old man presenting with body weight loss and exertional dyspnea. Highresolution computed tomography of the chest showed dense subpleural consolidation with traction bronchiectasis and volume loss predominantly in bilateral apical lesions and upper lobes. A histopathological analysis of a specimen of the right upper lobe showed histological patterns which were consistent with idiopathic pleuroparenchymal fibroelastotis (IPPFE). Treatment with pirfenidone was introduced with the expectation of its potential benefit. The effect of pirfenidone was satisfactory, and a decline in forced vital capacity was inhibitedduring treatment. This is the first case report suggesting the efficacy of pirfenidone for patients with IPPFE.
Journal Title
Internal Medicine
ISSN
13497235
Publisher
The Japanese Society of Internal Medicine
Volume
55
Issue
5
Start Page
497
End Page
501
Published Date
2016-03-01
Rights
Ⓒ 2016 The Japanese Society of Internal Medicine
EDB ID
DOI (Published Version)
URL ( Publisher's Version )
FullText File
language
eng
TextVersion
Publisher
departments
University Hospital
Medical Sciences