タカムラ, カズヒト Department of Digestive Surgery, Ehime Prefectural Central Hospital
ミヤケ, ヒデノリ Department of Surgery, Tokushima City Hospital
藤井, 正彦 Department of Digestive and Pediatric Surgery, Institute of Health Biosciences, The University of Tokushima Graduate School
ニシ, マサハル Department of Surgery, Tokushima Teisin Hospital
Angiomyolipoma (AML) is a rare benign tumor that occurs most commonly in the kidney. Lesions in the liver are usually solitary and multiple AMLs of the liver are extremely rare. Furthermore, extra renal or hepatic AML are rarely found. We report an unusual case of a 34-year-oldman with a solitary omental AML and multiple hepatic AMLs. At the age of 23, the patient underwent right nephrectomy and enucleation of a left renal tumor because of bilateral AMLs. At the age of 34, more than 6 lesions in the liver and an enlarged solitary omental AML were discovered. The omental tumor, 50×40mm, 49g,was extirpated it was well-defined and encapsulated a soft elastic mass. Histologically it was an epithelioid AML and positive for the melanogenesis-related marker HMB- 45, the same as the earlier right renal tumor. We describe the first case of a solitary omental AML, which had metastasized, and with more than 6 hepatic AMLs.
The journal of medical investigation : JMI
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