アクセス数 : ?
ダウンロード数 : ?
ID 111309
著者
Katsenos, Stamatis Army General Hospital of Athens|University Hospital of Ioannina
Nikolopoulou, Melita Army General Hospital of Athens
Rallis, Efstathios Army General Hospital of Athens
Constantopoulos, Stavros H University Hospital of Ioannina
キーワード
bronchoalveolar lavage
chronic eosinophilic pneumonia
neurofibromatosis-1
peripheral eosinophilia
資料タイプ
学術雑誌論文
抄録
Neurofibromatosis type 1 (formerly known as von Recklinghausen’s disease) is an autosomal dominant disorder, which results from the proliferation of the neural crest cells, thus affecting any organ system. Several pulmonary manifestations have hitherto been reported, including chest wall deformities, diffuse lung disease, thoracic neoplasms, pulmonary arterial hypertension, central hypoventilation, diaphragmatic paralysis and meningocele. However, eosinophilic lung disorders have not been described. An unusual case of chronic eosinophilic pneumonia in a patient with neurofibromatosis type 1, is reported herein. He had a propitious outcome, following corticosteroid treatment. This is the first well-documented case of chronic eosinophilic pneumonia and neurofibromatosis type 1 in the same patient. These clinical entities might share common pathogenic mechanisms, as suggested by the present study, that could explain their co-existence.
掲載誌名
The Journal of Medical Investigation
ISSN
13496867
13431420
cat書誌ID
AA11166929
AA12022913
出版者
Faculty of Medicine Tokushima University
56
1-2
開始ページ
64
終了ページ
69
並び順
64
発行日
2009-02
出版社版DOI
出版社版URL
フルテキストファイル
言語
eng
著者版フラグ
出版社版