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ID 115679
タイトル別表記
Clinical Guides for aHUS
著者
Kato, Hideki The University of Tokyo
Nangaku, Masaomi The University of Tokyo
Hataya, Hiroshi Tokyo Metropolitan Children’s Medical Center
Sawai, Toshihiro Shiga University of Medical Science
Ashida, Akira Osaka Medical College
Fujimaru, Rika Osaka City General Hospital
Hidaka, Yoshihiko Shinshu University
Kaname, Shinya Kyorin University
Maruyama, Shoichi Nagoya University
Yasuda, Takashi Kichijoji Asahi Hospital
Yoshida, Yoko The University of Tokyo
Ito, Shuichi Yokohama City University
Hattori, Motoshi Tokyo Women’s Medical University
Miyakawa, Yoshitaka Saitama Medical University
Fujimura, Yoshihiro Nara Medical University
Okada, Hirokazu Saitama Medical University
キーワード
alternative complement pathway
atypical hemolytic uremic syndrome
eculizumab
thrombotic microangiopathy
資料タイプ
学術雑誌論文
抄録
Atypical hemolytic uremic syndrome (aHUS) is a rare disease characterized by the triad of microangiopathic hemolytic anemia, thrombocytopenia, and acute kidney injury. In 2013, we developed diagnostic criteria to enable early diagnosis and timely initiation of appropriate treatment for aHUS. Recent clinical and molecular findings have resulted in several proposed classifications and definitions of thrombotic microangiopathy and aHUS. Based on recent advances in this field and the emerging international consensus to exclude secondary TMAs from the definition of aHUS, we have redefined aHUS and proposed diagnostic algorithms, differential diagnosis, and therapeutic strategies for aHUS.
掲載誌名
Pediatrics International
ISSN
1442200X
出版者
Japan Pediatric Society|Wiley
58
7
開始ページ
549
終了ページ
555
発行日
2016-07-26
権利情報
This is an open access article under the terms of the Creative Commons Attribution-NonCommercial License(https://creativecommons.org/licenses/by-nc/4.0/), which permits use, distribution and reproduction in any medium, provided the original work is properly cited and is not used for commercial purposes.
EDB ID
出版社版DOI
出版社版URL
フルテキストファイル
言語
eng
著者版フラグ
出版社版
部局
医学系